Sarcoma CDX Models

Explore Sarcoma CDX Models:

Model NameDescription
KHOS/NPOsteosarcoma model with p53 mutation and high metastatic potential; used to study chemoresistance and osteogenic differentiation pathways.
143BHighly aggressive osteosarcoma derived from the HOS line with KRAS transformation; TP53 mutant; widely used for metastasis and mitochondrial-targeted therapy studies.
SAOS-2Osteosarcoma model with homozygous TP53 deletion and RB1 mutation; non-metastatic, used in bone formation and mineralization research.
A204Rhabdomyosarcoma of epithelial origin; TP53 wild-type; sensitive to microtubule-targeting agents and used for pediatric soft tissue sarcoma studies.
Aska-SSSynovial sarcoma model with SS18-SSX1 fusion; biphasic histology; used for studies on translocation-driven sarcomagenesis and epigenetic therapies.
HS-SY-IIDerived from human synovial sarcoma with SS18-SSX1 fusion; epithelial morphology; utilized in testing HDAC and EZH2 inhibitors.
Yamato-SSSynovial sarcoma with SS18-SSX2 fusion transcript; monophasic spindle-cell subtype; used in fusion-driven oncogenesis and targeted therapy evaluation.
SJCRH30Alveolar rhabdomyosarcoma with PAX3-FOXO1 fusion; aggressive and metastatic; key model for testing targeted therapies in fusion-positive rhabdomyosarcoma.
SK-ES-1Ewing sarcoma model harboring EWSR1-FLI1 fusion; CD99-positive, highly proliferative; standard model for evaluating Ewing-specific targeted agents.